Hyperammonemia (or hyperammonaemia) is a metabolic disturbance characterised by an Hyperammonemia is one of the metabolic derangements that contribute to hepatic encephalopathy, which can cause swelling of astrocytes and. 31 jul. Doenças de depósito lisossômico (2 mucopolissacaridoses tipo 1; 1 suspeitos e confirmados de EIM, foi a hiperamonemia, seguida pela. Na tirosinemia hereditária ou tipo 1, além do tratamento dietético com Acidúria glutárica tipo 1 .. A hiperamonemia representa uma urgência metabólica.

Author: Mujar JoJogis
Country: Brunei Darussalam
Language: English (Spanish)
Genre: Relationship
Published (Last): 22 July 2015
Pages: 213
PDF File Size: 10.17 Mb
ePub File Size: 1.13 Mb
ISBN: 626-6-33494-432-2
Downloads: 26968
Price: Free* [*Free Regsitration Required]
Uploader: Arashigore

This page was last edited on 30 Septemberat Ammonia is a substance that contains nitrogen. Hyperammonemia is one of the metabolic derangements that contribute to hepatic encephalopathywhich can cause swelling of astrocytes and stimulation of NMDA-receptors in the brain.

An essential nutrient for the cat. The process is known as the urea cyclewhich comprises several enzymes acting in sequence. It is converted to the less toxic substance urea hiperxmonemia to excretion in urine by the kidneys.

Su deficiencia, se debe a la incapacidad del organismo de sintetizar la ornitina, un precursor de la arginina CASE et al. Abstract The present review analyses and updates the reader about domestic feline metabolism, through the following sections: Se requieren cofactores, como: Phenylbutyratewhich is the product of phenylacetate, conjugates with glutamine to form phenylacetylglutaminewhich is excreted by the kidneys.


Dietary protein, a metabolic source of ammonium, is restricted and caloric intake is provided by glucose and fat.

Obtenido en noviembre dedesde http: El acetil-CoA y el malonil-CoA, se condensan hiperamonemiia acetil-malonil. Contienen solamente apoproteina B Obtenido en agosto dedesde http: By using this site, you agree to the Terms of Use and Privacy Policy. Services on Demand Article. This is a treatment for hepatic encephalopathy. It is a product of the catabolism of protein. Carnosinemia Histidinemia Urocanic aciduria.

The present review analyses tippo updates the reader about domestic feline metabolism, through the following sections: Similarly, sodium benzoate reduces ammonia content in the blood by conjugating with glycine to form hippuric acidwhich is rapidly excreted by the kidneys. From Wikipedia, the free encyclopedia. The metabolic pathways that hiperamnoemia urea involve reactions that start in the mitochondria and then move into the cytosol. Hypervalinemia Isobutyryl-CoA dehydrogenase deficiency Maple syrup urine disease.

Amino acid metabolism disorders. Expert Consult – Online and Print.

It may be primary or secondary. GAMT deficiency Glycine encephalopathy.


Overstimulation of NMDA-receptors induces excitotoxicity. Hyperammonemia or hyperammonaemia is a metabolic disturbance characterised by an excess of ammonia in the blood. A brief review of the biochemistry of its requirement hiperamnoemia the clinical consequences of deficiency. Ocular albinism 1 Oculocutaneous albinism Hermansky—Pudlak syndrome Waardenburg syndrome.


How to cite this article. Methylmalonic acidemia Methylmalonyl-CoA mutase deficiency Propionic acidemia. Glutaric acidemia type 1 type 2 Hyperlysinemia Pipecolic acidemia Saccharopinuria. Views Read Edit View history. D ICD – Infobox medical condition new. hipframonemia


Acidification of the intestinal lumen using lactulose can decrease ammonia levels by protonating ammonia and trapping it in the stool.

J Feline Med Surg. La hidroximetilglutaril-CoA, es transformada a Mevalonato por la enzima hidroximetilglutaril-CoA-reductasa.

Histidine Carnosinemia Histidinemia Urocanic aciduria. Contienen las apoproteinas BE y C. It is a dangerous condition that may lead to brain injury and death. Treatment centers on limiting intake of ammonia and increasing its excretion.

Spanish pdf Article in xml format Article yipo How to cite this article Automatic translation Send this article by e-mail. Limusa Grupo Noriega Editores. Dopamine beta hydroxylase deficiency reverse: In other projects Wikimedia Commons. Intravenous arginine argininosuccinase deficiency sodium phenylbutyrate and sodium benzoate ornithine transcarbamoylase deficiency are pharmacologic agents commonly used as adjunctive therapy to treat hyperammonemia in patients with urea cycle enzyme deficiencies.